catalytic activity:Sulfite + O(2) + H(2)O = sulfate + H(2)O(2).,cofactor:Binds 1 protoheme group.,cofactor:Molybdenum (molybdopterin).,disease:Defects in SUOX are the cause of isolated sulfite oxidase deficiency (ISOD) [MIM:272300]; also known as sulfocysteinuria. ISOD is characterized by neurological abnormalities including multicystic leukoencephalopathy with brain atrophy. Patients often suffer from seizures. Often leads to death at an early age.,pathway:Energy metabolism; sulfur metabolism.,similarity:Contains 1 cytochrome b5 heme-binding domain.,subunit:Homodimer.,
Mitochondrion intermembrane space .
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